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科研机构
西安交通大学 [6]
厦门大学 [1]
上海药物研究所 [1]
中国科学院大学 [1]
复旦大学上海医学院 [1]
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期刊论文 [10]
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A trafficking-deficient KCNQ1 mutation, T587M, causes a severe phenotype of long QT syndrome by interfering with intracellular hERG transport.
期刊论文
Journal of cardiology, 2018
作者:
Wu Jie
;
Sakaguchi Tomoko
;
Takenaka Kotoe
;
Toyoda Futoshi
;
Tsuji Keiko
收藏
  |  
浏览/下载:5/0
  |  
提交时间:2019/11/26
Fluorescence resonance energy transfer
Patch-clamp
hERG
Long QT syndrome
KCNQ1-T587M
NS1643 enhances ionic currents in a G604S-WT hERG co-expression system associated with long QT syndrome 2
期刊论文
CLINICAL AND EXPERIMENTAL PHARMACOLOGY AND PHYSIOLOGY, 2017, 卷号: 44, 页码: 1125-1133
作者:
Huo, JianHua
;
Guo, Xueyan
;
Lu, Qun
;
Qiang, Hua
;
Liu, Ping
收藏
  |  
浏览/下载:3/0
  |  
提交时间:2019/11/26
hERG mutation
NS1643
patch-clamp
long QT syndrome
Propofol inhibits hERG K+ channels and enhances the inhibition effects on its mutations in HEK293 cells
期刊论文
EUROPEAN JOURNAL OF PHARMACOLOGY, 2016, 卷号: 791, 页码: 168-178
作者:
Han, Sheng-Na
;
Jing, Ying
;
Yang, Lin-Lin
;
Zhang, Zhao
;
Zhang, Li-Rong
收藏
  |  
浏览/下载:44/0
  |  
提交时间:2019/01/08
Propofol
QT prolongation
Human ether-a-go-go-related gene (hERG)
Protein trafficking
Gene mutation
Association of the hERG mutation with long-QT syndrome type 2, syncope and epilepsy
期刊论文
MOLECULAR MEDICINE REPORTS, 2016, 卷号: 13, 期号: [db:dc_citation_issue], 页码: 2467-2475
作者:
Li, Guoliang
;
Shi, Rui
;
Wu, Jine
;
Han, Wenqi
;
Zhang, Aifeng
收藏
  |  
浏览/下载:3/0
  |  
提交时间:2019/12/02
human ether-a-go-go-related gene
long-QT syndrome
whole-cell patch-clamp
mutation
trafficking
Pharmacological rescue of hERG currents carried out by G604S and wide type hERG co-expression
期刊论文
CLINICAL AND EXPERIMENTAL PHARMACOLOGY AND PHYSIOLOGY, 2016, 卷号: 43, 期号: [db:dc_citation_issue], 页码: 851-861
作者:
Huo, Jianhua
;
Zhang, Aifeng
;
Guo, Xueyan
;
Qiang, Hua
;
Liu, Ping
收藏
  |  
浏览/下载:3/0
  |  
提交时间:2019/12/02
hERG mutation
patch-clamp
G604S
long QT syndrome
Electrophysiological Characteristics of a SCN5A Voltage Sensors Mutation R1629Q Associated With Brugada Syndrome
期刊论文
http://dx.doi.org/10.1371/journal.pone.0078382, 2013
Zeng, Zhipeng
;
Zhou, Jieqiong
;
Hou, Yuxi
;
Liang, Xiaojing
;
Zhang, Ziguan
;
Xu, Xuejing
;
Xie, Qiang
;
Li, Weihua
;
Huang, Zhengrong
;
周洁琼
;
梁晓静
;
谢强
;
李卫华
;
黄峥嵘
收藏
  |  
浏览/下载:3/0
  |  
提交时间:2015/07/22
LONG QT SYNDROME
SODIUM-CHANNEL
DILATED CARDIOMYOPATHY
MOTION ABNORMALITIES
SLOW INACTIVATION
DOMAIN IV
CHANNELOPATHIES
FIBRILLATION
ACTIVATION
MECHANISMS
The EGFP/hERG fusion protein alter the electrophysiological properties of hERG channels in HEK293 cells
期刊论文
CELL BIOLOGY INTERNATIONAL, 2011, 卷号: 35, 期号: [db:dc_citation_issue], 页码: 193-199
作者:
Huang, Na
;
Lian, Jiang-Fang
;
Huo, Jian-Hua
;
Liu, Li-Ying
;
Ni, Lei
收藏
  |  
浏览/下载:3/0
  |  
提交时间:2019/12/10
long QT syndrome patch clamp
enhanced green fluorescent protein
hERG channel
confocal laser scanning microscope
Electrophysiological characterization of bmk 1, an alpha-like scorpion toxin, on rnav1.5 expressed in hek293t cells
期刊论文
Toxicology in vitro, 2008, 卷号: 22, 期号: 6, 页码: 1582-1587
作者:
Feng, Xing-Hua
;
Chen, Jue-Xu
;
Liu, Ying
;
Ji, Yong-Hua
收藏
  |  
浏览/下载:27/0
  |  
提交时间:2019/05/10
Hek293t cell
Cardiac sodium channels
Bmk i
Patch clamp
The G604S-hERG mutation alters the biophysical properties and exerts a dominant-negative effect on expression of hERG channels in HEK293 cells
期刊论文
PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY, 2008, 卷号: 456, 期号: 5, 页码: 917-928
作者:
Huo, Jianhua
;
Zhang, Yanmin
;
Huang, Na
;
Liu, Ping
;
Huang, Chen
收藏
  |  
浏览/下载:13/0
  |  
提交时间:2019/12/18
patch clamp
protein trafficking
hERG
mutation
long QT syndrome
Effect of mexiletine on long QT syndrome model
期刊论文
ACTA PHARMACOLOGICA SINICA, 2003, 卷号: 24, 期号: 4
作者:
Wang, HW
;
Zheng, YQ
;
Yang, ZF
;
Li, CZ
;
Liu, YM
收藏
  |  
浏览/下载:3/0
  |  
提交时间:2019/12/27
mexiletine
long QT syndrome
patch-clamp techniques
action potentials
electrocardiography
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